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A frequência da Anomalia de Ebstein encontrada foi semelhante a de outros Centros. A técnica de Cone foi viável na maior parte dos pacientes. A mortalidade. Ebstein’s anomaly is a malformation of the tricuspid valve. In this defect, there is a downward displacement of the tricuspid valve (located between the upper and. Antecedentes: en la actualidad, con la ecocardiografía fetal, es pos ble confirmar el diagnóstico in utero de la anomalía de Ebstein y determinar, con certeza.

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Check this box if you wish to receive a copy of your message. The third patient showed the greatest improvement Figure 3. Embryology and pathologic features of Ebstein’s anomaly.

Teratology, 50pp. Although associations between EA and certain genetic syndromes have been described, mainly trisomy 21 and WPW syndrome, 9,14 these syndromes were not found in the present series. Congenit Heart Dis, 9pp.

Orphanet: Anomalia de Ebstein

What Is Ebstein’s Anomaly? Ebstein’s malformation of the tricuspid valve: The documents contained in this web site are presented for information purposes only. Additional information Further information on this disease Classification s 3 Gene s 1 Clinical signs and symptoms Anomaliia in PubMed Other website s 3.

Br Heart J ; The patient with a permanent pacemaker was readmitted five months after surgery for pericardial effusion and minimal right pleural effusion and was discharged in NYHA class II seven days after readmission. This result contrasts with those of Anderson 9 and Da Silva, 15 who report a slight predominance of males, and with other studies that described no predominance of either gender. Natural history of Ebstein’s anomaly of tricuspid valve in childhood and adolescence.


Under a Creative Commons license. Ebstein’s Anomaly congenital heart defect ebsteins-anomaly. On a very rare case of insufficiency ebsteln the tricuspid valve caused by a severe congenital malformation of the same.

Anomalía de Ebstein en niños

A clinical case report. Transthoracic echocardiography is the most important diagnostic test for Ce, to determine TV morphology and physiology and to assess the cardiac chambers and the presence of other CHD.

Differential diagnosis The major differential diagnosis, particularly during fetal life, is dysplasia of the leaflets of the tricuspid valve. J Am Coll Cardiol ; Both sexes are equally affected.

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Clinical and echocardiographic features of Ebstein’s malformation in Sudanese patients. MyHealth for Mobile The MyHealth mobile app puts all your health information at your fingertips and makes managing your health care simple and quick.

A descriptive statistical analysis was performed absolute and relative frequencies, mean and standard deviation. At discharge, in this group two patients had no TR and three had mild TR.


Evolution of cardiothoracic index in the five patients undergoing cone reconstruction. The prevalence of EA found in this series was similar to other centers. Mean hospital stay was Ebstein’s malformation is a rare congenital cardiac anomaly characterized by rotational displacement of the septal and inferior leaflets of the tricuspid valve such that they are hinged within the right ventricle, rather than as expected anomaliaa the atrioventricular junction.

This study revealed that 0.

Chest X-rays showing an impressive reduction in cardiothoracic index after cone reconstruction. The authors have obtained the written informed consent of the patients or subjects mentioned in the article. Only comments written in English can be processed.

Antenatal diagnosis Antenatal diagnosis is now possible with fetal echocardiography that reveals hydrops fetalis. Evolution of cardiothoracic index in the five patients undergoing cone reconstruction. We aimed to describe the frequency, clinical profile, and early and short-term post-operative results in patients under the age of 18 years operated for this anomaly in a tertiary center in Angola.